Managing nutrition with Maple Syrup Urine Disease (MSUD) requires careful attention to protein intake and leucine restriction, as these amino acids cannot be properly processed by the body. Proper nutritional management is essential for preventing metabolic crises and supporting healthy growth and development. The resources below provide comprehensive guidelines, food lists, and practical tools developed by leading genetics and metabolic nutrition programs to help individuals with MSUD, families, and healthcare providers navigate the complexities of the MSUD diet. From detailed leucine content charts to cooking tips and meal planning strategies, these evidence-based resources offer the support needed to maintain optimal nutrition while managing this rare metabolic condition.
Comprehensive nutrition resources from Emory Genetics.
Detailed guidelines for healthcare professionals.
Reference guide for leucine and protein content in various foods.
Guide to low-protein food options for MSUD patients.
Recipes and cooking resources for low protein diets.
Video demonstration of low protein cooking techniques.
Discussion about managing relationships while on a low protein diet.
Guidelines for safe exercise with MSUD.
Mobile app for tracking protein intake and managing MSUD diet (available for a modest fee).